Pulmonary​

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• Cure CMD Pulmonary Function Testing

• Anesthesia and Ullrich Congenital Muscular Dystrophy: Comment, Veyckemans, 2021

• Randomized trial of lung hyperinflation therapy in children with congenital muscular dystrophy, Sawnani, 2020

• Transition of patients with neuromuscular disease and chronic ventilator-dependent respiratory failure from pediatric to adult pulmonary care, Cheng, 2020

• Non-invasive Ventilation in Children With Neuromuscular Disease, Fauroux, 2020

• Anaesthesia and neuromuscular disorders: what a neurologist needs to know, Bresselaar, 2020

• Numerical Analysis of Airway Mucus Clearance Effectiveness Using Assisted Coughing Techniques, Ran, 2020

• Respiratory Involvement in Patients with Neuromuscular Diseases: A Narrative Review, Voulgaris, 2019

• Non-invasive ventilation during surgery under neuraxial anesthesia: a pathophysiological perspective on application and benefits and a systematic literature review, Corcione, 2019

• Breathe DMD!, Mayer 2018

• Detection of early nocturnal hypoventilation in neuromuscular disorders, Trucco, 2018

• Respiratory Care in Neuromuscular Diseases, Sahni, 2018

• A novel feature extraction technique for pulmonary sound analysis, Mondal, 2018

• Sleep-Disordered Breathing in Neuromuscular and Chest Wall Diseases, Hilbert, 2018

• Neuromuscular disorders and chronic ventilation, Alexiou, 2018

• Airway clearance techniques in neuromuscular disorders: A state of the art review, Chatwin, 2018

• Airway clearance techniques in neuromuscular disorders, Toussaint, 2018

• Imaging of respiratory muscles in neuromuscular disease: A review, Harlaar, 2018

• Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo-mouse model of FKRP-deficient muscular dystrophy, Yu, 2018

• Airway clearance techniques in neuromuscular disorders: A state of the art review, Chatwin, 2018

• Invasive versus non-invasive ventilation for acute respiratory failure in neuromuscular disease and chest wall disorders, Luo, 2017

• Neuromuscular scoliosis complication rates from 2004 to 2015: a report from the Scoliosis Research Society Morbidity and Mortality database, Cognetti, 2017

• Long-term non-invasive ventilation in muscular dystrophy, Kinnear, 2017

• Management of acute neuromuscular disorders, Wijdicks, 2017

• Prognostic value of nocturnal hypoventilation in neuromuscular patients, Ojlikowski, 2017

• Respiratory complications, management and treatments for neuromuscular disease in children, Buu, 2017

• Effect of expiratory positive airway pressure on tidal volume during non-invasive ventilation, Kinnear, 2017

• Update on the respiratory management of patients with chronic neuromuscular disease, Priou, 2017

• Mouthpiece ventilation and complementary techniques in patients with neuromuscular disease: A brief clinical review and update, Pinto, 2017

• The clinical use of mechanical insufflation-exsufflation in children with neuromuscular disorders in Europe, Hoy, 2017

• Patient Preferences for Treatments of Neuromuscular Diseases: A Systematic Literature Review, Landfeldt, 2017

• Effect of Noninvasive Ventilation on Tracheal Reintubation Among Patients with Hypoxemic Respiratory Failure Following Abdominal Surgery, Jaber, 2016

• Respiratory failure because of neuromuscular disease, Howard, 2016

• Noninvasive ventilation for neuromuscular respiratory failure, Rabinstein, 2016

• Home Mechanical Ventilation: An Overview, Simonds, 2016

• Prognostic Value of Initial Assessment of Residual Hypoventilation Using Nocturnal Capnography in Mechanically Ventilated Neuromuscular Patients: A 5-Year Follow-up Study, 2016

• Hereditary Myopathies with Early Respiratory Insufficiency in Adults, Naddaf, 2016

• Respiratory Muscle Weakness and Respiratory Failure in Pediatric Neuromuscular Disorders: The Value of Nonivasive Determined Tension-Time Index, Stehling, 2016

• Orthognathic Surgery in Patients With Congenital Myopathies and Congenital Muscular Dystrophies: Case Series and Review of the Literature, Bezak, 2016

• Noninvasive Mechanical Ventilation Improves Breathing-Swallowing Interaction of Ventilator Dependent Neuromuscular Patients: A Prospective Crossover Study, Garguilo, 2016

• Clinical Outcomes Associated with Home Mechanical Ventilation: A Systematic Review, MacIntyre, 2016

• The Role of Noninvasive Ventilation in Patients with "Do Not Intubate" Order in the Emergency Setting, Vilaca, 2016

• Noninvasive airway approaches for acute neuromuscular respiratory failure in emergency departments, Chen, 2016

• Adherence and Barriers to Hyperinsufflation in Children With Congenital Muscular Dystrophy, Pascoe, 2016

• Facilitators and Barriers to Noninvasive Ventilation Adherence in Youth with Nocturnal Hypoventilation Secondary to Obesity or Neuromuscular Disease, Ennis, 2015

• Diagnosis of muscle diseases presenting with early respiratory failure, Pfeffer, 2015

• Efficacy of mechanical insufflation-exsufflation in extubating unweanable subjects with restrictive pulmonary disorders, Bach, 2015

• Emergency Neurological Life Support: Acute Non-traumatic Weakness, Flower, 2015

• Sleep-disordered Breathing in Neuromuscular Disease, Aboussouan. 2015

• Impact of Hyperglycemia in the Outcome of Patients with Primary Neuromuscular Respiratory Failure, Cabrera-Serrano, 2015

• Muscle impairment in neuromuscular disease using an expiratory/inspiratory pressure ratio, Fregonezi, 2015

• Invasive home mechanical ventilation: living conditions and health-related quality of life, Huttmann, 2015

• Lifestyle Implications of Home Mechanical Insufflation-Exsufflation for Children With Neuromuscular Disease and Their Families, Moran, 2015

• Long Term Non-Invasive Ventilation in Children: Impact on Survival and Transition to Adult Care, Chatwin, 2015

• Neuromuscular disorders and sleep in critically ill patients, Irfan, 2015

• Home Mechanical Ventilation in Childhood-Onset Hereditary Neuromuscular Diseases: 13 Years' Experience at a Single Center in Korea, Han, 2015

• Use of mechanical airway clearance devices in the home by people with neuromuscular disorders: effects on health service use and lifestyle benefits, Mahede, 2015

• Pulmonary Manifestations of Neuromuscular Diseases, Khatwa, 2015

• Can daytime measures of lung function predict respiratory failure in children with neuromuscular disease, Pandit, 2015

• Mechanical Insufflation-Exsufflation: The Good, the Bad, and the Ugly, Willis, 2015

• Noninvasive Ventilation Adherence in Youth with Nocturnal Hypoventilation Secondary to Obesity or Neuromuscular Disorder: It Takes a Village, 2015, Yuan

• Respiratory pathophysiology in congenital muscle disorders: implications for pro-active care and clinical research, Rutkowski, 2015

• Extubation Protocol, 2014

• Air stacking: effects on pulmonary function in patients with spinal muscular atrophy and in patients with congenital muscular dystrophy, Marques, 2014

• Diaphragmatic dysfunction in Collagen VI myopathies, Quijano-Roy, 2014

• Total intravenous anesthesia for a patient with Fukuyama congenital muscular dystrophy undergoing scoliosis surgery, Matsuda, 2014

• Anesthesia Recommendations for Patients Suffering from Merosin-deficient congenital muscular dystrophy, Orphanet, 2013

• Respiratory Advice- Scoliosis- For patients with myotubular and centronuclear myopathy and other congenital myopathies, 2012

• British Thoracic Society guideline for respiratory management of children with neuromuscular weakness, Hull, 2012

• Guidance on breathing and non-invasive Ventilation for Children from the age of two years old living with a neuromuscular condition, 2012

• Screening for Sleep-Disordered Breathing in Neuromuscular Disease Using a Questionnaire for Symptoms Associated with Diaphragm Paralysis, Steier, 2010

• Should Patients with Neuromuscular Disease Be Denied the Choice of the Treatment of Mechanical Ventilation, Rumbak, 2009

• Pulmonary Function Testing in Neuromuscular Disorders, Sharma, 2009

• Families of SMA, Breathing Basics, 2009

• Cough Assist-A patient guide, Philips Respironics, 2009

• Equipment Options for Cough Augmentation, Ventilation, and Noninvasive Interfaces in Neuromuscular Respiratory Management, Boitano, 2009

• Extubation of Patients with Neuromuscular Weakness- A New Management Paradigm, Bach, 2009

• The Pathophysiology of Respiratory Impairment in Pediatric Neuromuscular Diseases, Panitch, 2009

• Initiating Noninvasive Management of Respiratory Insufficiency in Neuromuscular Disease, Benditt, 2009

• American College of Chest Physicians Consensus Statement on the Respiratory and Related Management of Patients With Duchenne Muscular Dystrophy, Birnkrant, 2007

• Mental Health of Mothers Caring for Venilator-Assisted Children at Home, Kuster, 2006

• Mechanical insufflation/exsufflation- Has it come of age? - A commentary, Bach, 2003

• Safe Swallowing Advice, Bagnall